Cystic Fibrosis: A Chronic Illness

Cystic Fibrosis: A Chronic Illness

Introduction

Cystic Fibrosis is a disease that affects both children and adults. Sometimes back, the condiction affected people a lot and caused deaths (Connett, 2016). However, due to the improved techlogy, the rate in which deaths are encountered has reduced. Treatment has been taken to another level to stand with victims and make sure they live longer (Hommel et al., 2019).

Pathophysiology of Disease

Cystic Fibrosis is an autosomal recessive disorder that affects about 30,000 children and adults in the United States (Porth & Matfin, 2014). The mutation occurs on the long arm of chromosome 7, which encodes for the cystic fibrosis transmembrane regulator (CFTR). The CFTR protein regulates the function of chloride and sodium channels at the surface of epithelial cells. Although both chloride and sodium are regulated and affected by the CFTR protein, abnormal chloride movement appears to be the primary defect of the mutation (Hockenberry, Wilson, and Rodgers, 2017).

Most of the people with cystic fibrosis in the inclusion of the adults are not diagnosed since they missed screening when they were young. Complications that are linked with cystic fibrosis and likely to be recognized in primary care include liver disease and reduced mineral density of the bones. The condition commonly does not have a cure but can be minimized through various means like exercise (Connett, 2016). Overall disease effects on the respiratory, gastrointestinal system & reproductive. However, there is an advanced treatment of the diseases, and most of the people with it are likely to live longer when they follow the right strategies.

Effects on growth and development

CF keeps children from getting nutrients and calories needed from the food. Due to this, children with CF their weight is not average. Failure to have healthy weight exposes the children to a risk of other health issues and might affect them from living for a long time. Mostly, the disease affects the digestive tract and lungs, causing thick mucus build-up in the lungs, which causes breathing issues. Consequently, malnutrition risk increases and results in the delayed development in CF patients.

Findings

Findings from the article showed a positive relationship between the lung function and the BMI ongoing above 50^th centile (Connett, 2016). This finding did not raise concern on the level in which prevailing opinions about eating habits should be modified to impact the outcome portion. Another critical finding which Connett developed was that medical interventions to upgrade nutritional status are restricted to modifications of enzyme doze or acid suppression care (Connett, 2016). The findings indicated the relevance of reevaluating the use of the best strategies to promote healing. Also, the results further explained on non-adherence as a challenge in treating CF. This means that there are people who don’t follow what they are told to do after been diagonalized.

Ashkenazi et al.  emphasized on the relevance of screening new-born and advance nutritional implementation for cystic fibrosis patients (Ashkenazi et al., 2019). The findings stressed the need for mastering nutrition at an early age as a way of preventing outcomes in the future. Based on the findings, when BMI is low at an early age, there is a possibility of lung transplantation. The nurse should carefully analyze patients to identify patients who might be malnourished. Ashkenazi et al. further explained that screening of the sigs in an early stage might help in using the information obtained for future treatment.

There are various challenges that nurses face when trying to make people adhere to the rules of minimizing the disease occurrence (Hommel et al., 2019). The problems, though, helps in knowing what a patient wants precisely. Hommel et al. further suggested that the challenges faced not only make the nurse lose the battle but make them more flexible. The study done indicated that almost 41% of the children did not follow the calories intake process.

Implementation of findings

It’s the responsibility of the nurse to ensure that patients are comfortable. Due to the increasing use of modern things, even modern foods have emerged which, when consumed for a long time, makes people have complications in the future (Ashkenazi et al., 2019). It’s, therefore, suitable for the nurses to use necessary means to teach people on best food they should consume.

Nurses can as well use necessary means of technology to get to know about various ways in which nutrition can be promoted. The technique implemented by setting seminars for the victims of the disease and the entire society (Ashkenazi et al., 2019). The training will offer the best solutions to many people who might be worried about the best treatment and relevance of preventing the disease.

Most of the time, people don’t follow up or even don’t show commitment to their condition.  Nurses should make sure people use compelling ways to follow the requirements for healthy living. This can be made possible if nurses will educate the patients (Connett, 2016). It’s good for the nurses to press on setting program which will help the entire society know about the best diet and what they should strictly follow for their benefits.  Nurses are required to conduct screening when the children are just infants. This can be implemented by doing testing immediately after birth. This will help to reduce the rate of deaths, which occurs at a late stage. Nurses can as well advise the parents with CF on what they should do to keep their new-born protected (Connett, 2016). The plan helps not only the present victims but also for handling other patients in the future.

In hospitals, nurses face different challenges since some patients are malnourished. A program can be developed to help in recognizing such conditions when they occur. It’s good for the nurse to keep the patients on track by mastering those with serious issues that need attention (Connett, 2016). When the patients are identified, they should be put in a system where the nurse will find it easy to look at such patients and monitor their recovery processes.

Parse to Patient Care

Parse’s theory guides nurses to concentrate on the relevance of life. Human becoming theory rates life quality from one person to another based on their perceptions. There is a transformative strategy for all nursing levels (Parse,2014). The approach helps nurses to know about their opinions and what they need. This guides nursing is handling a different kind of patients and who want distinct help. When dealing with a patient, the primary purpose is to save a life. Following, they help the nurse to have enough knowledge about what to do and steps to undertake to deal with every nurse equally.

Integration of faith

Faith clearly described as an aspect of nursing care.  Applies directly to the needs of patient.  Connection between faith and interventions highly evident (2).

Conclusion

Cystic Fibrosis disease can be prevented, but offering full treatment is not guaranteed. However, to cure the illness, both patients and the nurse should participate. The nurse should ensure every patient is dealt with carefully to save a life. Despite there are different things because Cystic Fibrosis can be prevented. Based on the articles, the treatment of the disease has improved, and the number of deaths is minimized.

References

Ashkenazi, M., Sarouk, I., Aluma, B. E. B., Dagan, A., Bezalel., Keler,S…Nathan, N. (2019).

Nutritional Status in Childhood as a Prognostic Factor in Patients with Cystic Fibrosis. Lung, 197(3), 371-376. https://doi-org.libproxy.calbaptist.edu/10.1007/s00408-019-00218-3

Connett, G. J. (2016). Cystic Fibrosis Nutrition—Chewing the Fat. Paediatric Respiratory

Reviews, 17, 42-44. https://doi-org.libproxy.calbaptist.edu/10.1016/j.prrv.2015.08.006

Hockenberry, M. J., Wilson, D., & Rodgers, C. C. (2017). Wongs essentials of pediatric nursing. St. Louis, MO: Elsevier.

Hommel, K. A., Rausch, J., Towner, E. K., Schall, J., Maqbool, A., Mascarenhas, M., &

Stallings, V. (2019). Adherence to Nutritional Supplementation in Cystic Fibrosis. Journal of Pediatric Nursing, 47, 18-22. https://doi-org.libproxy.calbaptist.edu/10.1016/j.pedn.2019.04.011

Parse, R. R. (2014). The humanbecoming paradigm: A transformational worldview.

Pittsburgh, PA: Discovery International Publications.

Porth, C. M., & Matfin, G. (2014). Pathophysiology: Concepts of altered health sciences. Philadelphia, PA: Lippincott Williams & Wilkins.